Cloacal malformation combined with multiple malformations
https://doi.org/10.31146/1682-8658-ecg-233-1-143-147
Abstract
Multiple congenital malformations (MVP) are conditions when there is a violation of the structure and functioning of at least two organs or systems. They do not shorten life expectancy, but reduce its quality, require constant monitoring by specialists or certain conditions of detention. The most difficult malformation of the anorectal region in girls is a congenital cloaca - the fusion of the urethra, vagina and rectum into a single channel that opens in the genital fissure at the site of the external opening of the urethra or vagina. Often, patients with cloacal malformations often have associated VACTERLS abnormalities, which relate to abnormalities in structures originating from the embryonic mesoderm and tend to co-occur. The treatment of such patients requires the attention of specialists from several industries and constant supervision. This clinical case highlights the need for careful planning and coordination of the efforts of specialists from various fields of medicine for the successful management of patients with such complex malformations. Modern approaches to treatment, prognosis and possibilities for improving the quality of life of patients with cloacal malformation and associated anomalies are discussed.
About the Authors
E. V. Sibirskaya
N.I. Pirogov Russian National Research Medical University; Russian Children’s Clinical Hospital (RCCH) is a branch of the Federal State Autonomous Educational Institution of Higher Education, the Pirogov Russian National Research Medical University of the Ministry of Health of the Russian Federation; Russian University of Medicine
Russian Federation
Russian Federation
I. V. Karachentsova
N.I. Pirogov Russian National Research Medical University; Russian Children’s Clinical Hospital (RCCH) is a branch of the Federal State Autonomous Educational Institution of Higher Education, the Pirogov Russian National Research Medical University of the Ministry of Health of the Russian Federation
Russian Federation
Russian Federation
P. O. Nikiforova
N.I. Pirogov Russian National Research Medical University; Russian Children’s Clinical Hospital (RCCH) is a branch of the Federal State Autonomous Educational Institution of Higher Education, the Pirogov Russian National Research Medical University of the Ministry of Health of the Russian Federation
Russian Federation
Russian Federation
Yu. A. Kirillova
N.I. Pirogov Russian National Research Medical University; Russian Children’s Clinical Hospital (RCCH) is a branch of the Federal State Autonomous Educational Institution of Higher Education, the Pirogov Russian National Research Medical University of the Ministry of Health of the Russian Federation
Russian Federation
Russian Federation
K. I. Alamkina
Sechenov University
Russian Federation
Russian Federation
References
1. Fernando M.A., Creighton S.M., Wood D. The long-term management and outcomes of cloacal anomalies. Pediatric Nephrology. 2015 May;30(5):759-65. doi: 10.1007/s00467-014-2875-7.
2. Adamyan L.V., Sharkov S.M., Sibirskaya E.V., Pivazyan L.G., Avetisyan D.S. Persistent cloaca in the gynecologist’s practice (a literature review). Detskaya khirurgiya (Russian Journal of Pediatric Surgery). 2021; 25(5): 315-319. (in Russ.) doi: 10.18821/1560-9510-2021-25-5-315-319.@@ Адамян Л.В., Шарков С.М., Сибирская Е.В., Пивазян Л.Г., Аветисян Д.С. Персистирующая клоака в практике врача-гинеколога (обзор литературы). Детская хирургия. 2021; 25(5): 315-319. doi: 10.18821/1560-9510-2021-25-5-315-319.
3. Adamyan L.V., Sibirskaya E.V., Pivazyan L.G., Avetisyan Ju.S. Long-term gynecological outcomes in patients with persistent cloaca.Russian Journal of Human Reproduction. 2022;28(1):81-86. (In Russ.) doi: 10.17116/repro20222801181.@@ Адамян Л.В., Сибирская Е.В., Пивазян Л.Г., Аветисян Д.С. Долгосрочные гинекологические исходы у пациенток с персистирующей клоакой. Проблемы репродукции. 2022;28(1):81-86. doi: 10.17116/repro20222801181.
Review
For citations:
Sibirskaya E.V., Karachentsova I.V., Nikiforova P.O., Kirillova Yu.A., Alamkina K.I. Cloacal malformation combined with multiple malformations. Experimental and Clinical Gastroenterology. 2025;(1):143-147. (In Russ.) https://doi.org/10.31146/1682-8658-ecg-233-1-143-147
Views:
117
Email this article 