Liver involvement in systemic AL amyloidosis
https://doi.org/10.31146/1682-8658-ecg-230-10-229-235
Abstract
The article presents a clinical case of late diagnosis of systemic AL amyloidosis. Severe hepatomegaly, cholestasis syndrome combined with progressive heart failure and nephrotic syndrome prompted the patient to be examined for systemic amyloidosis. This observation demonstrates the need for knowledge of gastroenterologic and systemic manifestations of amyloidosis, algorithms for diagnosing the disease in order to timely identify such patients, prescribe effective chemotherapy to increase the life expectancy of patients.
About the Authors
A. A. Markova
Saratov State Medical University named after V.I. Razumovsky
Russian Federation
Russian Federation
E. I. Kashkina
Saratov State Medical University named after V.I. Razumovsky
Russian Federation
Russian Federation
E. V. Grigoryeva
Saratov State Medical University named after V.I. Razumovsky
Russian Federation
Russian Federation
A. V. Aparkina
Saratov State Medical University named after V.I. Razumovsky
Russian Federation
Russian Federation
E. V. Voloshinova
Saratov State Medical University named after V.I. Razumovsky
Russian Federation
Russian Federation
O. A. Vorobyeva
National Center of Clinical Morphological Diagnostics
Russian Federation
Russian Federation
References
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Review
For citations:
Markova A.A., Kashkina E.I., Grigoryeva E.V., Aparkina A.V., Voloshinova E.V., Vorobyeva O.A. Liver involvement in systemic AL amyloidosis. Experimental and Clinical Gastroenterology. 2024;(10):229-235. (In Russ.) https://doi.org/10.31146/1682-8658-ecg-230-10-229-235
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