Hilaiditi syndrome as a cause of chronic duodenal obstruction in children operated on for omphalocele
https://doi.org/10.31146/1682-8658-ecg-192-8-181-187
Abstract
Introduction. Chilaiditi syndrome—hepatodiaphragmatic interposition—is a rare condition in which bowel loops are compressed in the space between the liver and the dome of the diaphragm, which can lead to the development of a wide range of complications. In the available literature data on the clinical manifestations of this condition in children with omphalocele are not described.
Materials and methods. The article describes rare clinical cases of patients 1 year 1 month, 2 years 11 month and 12 years old, previously operated on in the neonatal period for omphalocele, in whom, in the long term after surgery, signs of hepatodiaphragmatic interposition persisted, which led to the development of chronic duodenal obstruction.
Conclusion: It has been proven that the leading role in restoring the normal topography of the abdominal organs in children with omphalocele is played by the complete mobilization of the liver and the great vessels (IVC) fi xing it, which provide the possibility of its subphrenic localization. Chronic duodenal obstruction in children with a similar pathology has not been previously described. The proposed original method of surgical treatment seems to be pathogenetically justifi ed.
About the Authors
A. Yu. Razumovskiy
Pirogov Russian National Research Medical University; Filatov Children City Clinical Hospital, st. Sadovaya- Kudrinskaya
Russian Federation
Russian Federation
Alexander Yu. Razumovsky, Corresponding Member of the Russian Academy of Sciences, Doctor of Medical Sciences,
Professor of the Department of Pediatric Surgery; head of the thoracic department, doctor-pediatric surgeon; Chief
Pediatric Surgeon of the Moscow Department of Health, Chief Freelance Pediatric Surgeon of the Central Federal District of
the Russian Federation
st. Sadovaya- Kudrinskaya, 15, Moscow
N. V. Kulikova
Filatov Children City Clinical Hospital, st. Sadovaya- Kudrinskaya
Russian Federation
Russian Federation
Nadezhda V. Kulikova, doctor -pediatric surgeon
15, Moscow, 123001
V. V. Cholostova
Pirogov Russian National Research Medical University; Filatov Children City Clinical Hospital, st. Sadovaya- Kudrinskaya
Russian Federation
Russian Federation
Victoria V. Cholostova, Dr. Sci (Med.), associate professor of the Department of Pediatric Surgery; Pediatric surgeon
15, Moscow, 123001
M. A. Amanova
Pirogov Russian National Research Medical University
Russian Federation
Russian Federation
Maisa A. Amanova, postgraduate student of the Department of Pediatric Surgery, Pediatric Faculty
Moscow
A. I. Khavkin
Veltischev Research and Clinical Institute for Pediatrics of the Pirogov Russian National Research Medical University
Russian Federation
Russian Federation
Anatoly I. Khavkin, MD, PhD, Dr Sci (Med), Prof., Ch. Chief Researcher of the Department of Gastroenterology
Moscow
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Review
For citations:
Razumovskiy A.Yu., Kulikova N.V., Cholostova V.V., Amanova M.A., Khavkin A.I. Hilaiditi syndrome as a cause of chronic duodenal obstruction in children operated on for omphalocele. Experimental and Clinical Gastroenterology. 2021;(8):181-187. (In Russ.) https://doi.org/10.31146/1682-8658-ecg-192-8-181-187
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