Hereditary type V hyperlipidemia as an etiological factor of severe necrotizing pancreatitis
https://doi.org/10.31146/1682-8658-ecg-233-1-154-158
Abstract
Acute pancreatitis (AP) remains a relevant issue in pediatric surgery. One of the risk factors for the development of AP is hereditary hypertriglyceridemia, which is often diagnosed only at the time of AP exacerbation. This article presents a clinical case of necrotizing pancreatitis of a 16-year-old girl with hereditary hypertriglyceridemia (type V hyperlipidemia). The management strategy for the child is described, with a comprehensive overview of diagnostic and therapeutic measures taken. Emphasis is placed on the main mechanisms of the inflammatory process’s pathogenesis. The necessity of timely diagnosis of lipid metabolism disorders and identifying factors contributing to AP development is highlighted to prevent potentially life-threatening conditions.
About the Authors
D. A. Pyhteev
Moscow Region Research and Clinical Institute n. a. M.F. Vladimirskiy
Russian Federation
Russian Federation
L. M. Elin
Moscow Region Research and Clinical Institute n. a. M.F. Vladimirskiy
Russian Federation
Russian Federation
T. A. Bokova
Moscow Region Research and Clinical Institute n. a. M.F. Vladimirskiy; N.I. Pirogov Russian National Research Medical University
Russian Federation
Russian Federation
M. R. Globa
Moscow Region Research and Clinical Institute n. a. M.F. Vladimirskiy
Russian Federation
Russian Federation
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Review
For citations:
Pyhteev D.A., Elin L.M., Bokova T.A., Globa M.R. Hereditary type V hyperlipidemia as an etiological factor of severe necrotizing pancreatitis. Experimental and Clinical Gastroenterology. 2025;(1):154-158. (In Russ.) https://doi.org/10.31146/1682-8658-ecg-233-1-154-158
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