Cholelithiasis in a patient with hereditary spherocytosis
https://doi.org/10.31146/1682-8658-ecg-218-10-229-233
Abstract
The article presents a clinical observation of a patient with hereditary hemolytic anemia and cholelithiasis that developed from it. The record of ultrasound of the abdominal, magnetic resonance cholangiopancreatography, and the movement of laboratory parameters are demonstrated. The patient underwent splenectomy with cholecystectomy, the information of the postoperative period are presented. The purpose of the article was to study, using the example of this clinical case, the features of the course of hereditary spherocytosis complicated by cholelithiasis in an adult patient; to assess the feasibility of the presented variant of the tactics of managing patients with this pathology. It is shown that at the present stage, despite the dynamic pace of development, pharmacology does not offer effective therapy, and splenectomy remains the only method for treating hereditary spherocytosis. Removal of the spleen eliminates intrasplenic hemolysis and therefore corrects the anemia. With the development of gallstone disease as a result of hemolysis, splenectomy is performed in combination with cholecystectomy.
About the Authors
A. E. Shklyaev
Izhevsk State Medical Academy; First republican Clinical Hospital
Russian Federation
Russian Federation
V. V. Zaitseva
Izhevsk State Medical Academy
Russian Federation
Russian Federation
A. G. Bessonov
First republican Clinical Hospital
Russian Federation
Russian Federation
V. M. Dudarev
Izhevsk State Medical Academy
Russian Federation
Russian Federation
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Review
For citations:
Shklyaev A.E., Zaitseva V.V., Bessonov A.G., Dudarev V.M. Cholelithiasis in a patient with hereditary spherocytosis. Experimental and Clinical Gastroenterology. 2023;(10):229-233. (In Russ.) https://doi.org/10.31146/1682-8658-ecg-218-10-229-233
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